RHABDOID VARIANT OF CLEAR CELL RENAL CELL CARCINOMA– A CASE REPORT

Rhabdoid Variant Renal Cell Carcinoma

Abstract

INTRODUCTION

Renal cell carcinoma (RCC) accounts for 2% of all malignancies and over 90% of all renal malignancies. It is a tumour of adults with an average age at diagnosis of 55-60 years and a male to female ratio of 2:1. Of the various histological subtypes, clear cell type is the most common¹. Rhabdoid tumour is a malignant tumour of the kidney which occurs typically in children, however only a few cases of pure rhabdoid tumours have been reported in adults². Rhabdoid variant of clear cell renal cell carcinoma also known as adult clear cell renal cell carcinoma with rhabdoid features is an uncommon tumor in adults. Literature shows that about 5% of the renal cell carcinomas exhibit rhabdoid features. Moreover, it is a high grade neoplasm with aggressive behaviour and a dismal outcome³.