AUTOSOMAL DOMINANT HYPER IGESYNDROME (JOB’S SYNDROME): A CASE REPORT OF TWO PATIENTS

Authors

  • Saima Gillani Ayub Medical College, Abbottabad Pakistan
  • Farida Aziz Frontier Medical College Abbottabad Pakistan
  • Burhan Ali Danish Ayub Teaching Hospital, Abbottabad Pakistan
  • Attia Iqbal Ayub Teaching Hospital, Abbottabad Pakistan
  • Muhammad Junaid Khan Ayub Teaching Hospital, Abbottabad Pakistan

Keywords:

Immunodeficiency, Job’s syndrome, Hyper IgE syndrome

Abstract

Recently we came across two male patients with Hyper IgE type immune deficiency (HIES/Job’s syndrome), a primary immune deficiency disorder characterized by abnormally raised serum levels of IgE and repeated childhood infections. In our hospital in pediatrics and nursery, acquired immunodeficiency secondary to severe malnutrition, prolonged steroid therapy, nephrotic syndrome, aplastic anemia, leishmaniasis, leukemias and other malignancies is more common as compared to inherited causes.

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Published

27-01-2020

Issue

Vol. 70 No. Suppl-1 (2020): January Suppl-1

Section

Case Reports

How to Cite

1.
Gillani S, Aziz F, Danish BA, Iqbal A, Khan MJ. AUTOSOMAL DOMINANT HYPER IGESYNDROME (JOB’S SYNDROME): A CASE REPORT OF TWO PATIENTS. Pak Armed Forces Med J [Internet]. 2020 Jan. 27 [cited 2024 Nov. 7];70(Suppl-1):S193-95. Available from: https://pafmj.org/PAFMJ/article/view/3820