PENTALOGY OF CANTRELL WITH ECTOPIA CORDIS: A RARE CONGENITAL ABNORMALITY
Abstract
The link of sternal fusion defects with many cardiac, diaphragmatic, and anterior body wall defects represents developmental field complex that includes the Pentalogy of Cantrell (PC) and Ectopia Cordis (EC). Attempts of surgical repair leads to survival of few numbers of patients and the main causes of death in these patients include tachycardia, bradycardia, hypotension, rupture of the diverticulum, and failure of heart. We report a diagnostic case of PC ina 12-hour baby girl in AFIC/NIHD Rawalpindi.