AUTOSOMAL DOMINANT HYPER IGESYNDROME (JOB’S SYNDROME): A CASE REPORT OF TWO PATIENTS

  • Saima Gillani Ayub Medical College, Abbottabad Pakistan
  • Farida Aziz Frontier Medical College Abbottabad Pakistan
  • Burhan Ali Danish Ayub Teaching Hospital, Abbottabad Pakistan
  • Attia Iqbal Ayub Teaching Hospital, Abbottabad Pakistan
  • Muhammad Junaid Khan Ayub Teaching Hospital, Abbottabad Pakistan
Keywords: Immunodeficiency, Job’s syndrome, Hyper IgE syndrome

Abstract

Recently we came across two male patients with Hyper IgE type immune deficiency (HIES/Job’s syndrome), a primary immune deficiency disorder characterized by abnormally raised serum levels of IgE and repeated childhood infections. In our hospital in pediatrics and nursery, acquired immunodeficiency secondary to severe malnutrition, prolonged steroid therapy, nephrotic syndrome, aplastic anemia, leishmaniasis, leukemias and other malignancies is more common as compared to inherited causes.

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Published
2020-01-27
How to Cite
Gillani, S., Aziz, F., Danish, B., Iqbal, A., & Khan, M. (2020). AUTOSOMAL DOMINANT HYPER IGESYNDROME (JOB’S SYNDROME): A CASE REPORT OF TWO PATIENTS. Pakistan Armed Forces Medical Journal, 70(Suppl-1), S188-90. Retrieved from https://pafmj.org/index.php/PAFMJ/article/view/3820