Surgical Experiences and Results of the Management of Double Chambered Right Ventricle

Mujahid Razzaq; Salman Ahmed Shah; Saeedah Asaf; Muhammad Asim Khan; Tehmina Kazmi; Uzma  Kazmi

doi:10.51253/pafmj.v74i3.5464

Authors

Mujahid Razzaq Department of Pediatrics, Children Hospital and Institute of Child Health, Lahore Pakistan
Salman Ahmed Shah Department of Pediatrics, Children Hospital and Institute of Child Health, Lahore Pakistan
Saeedah Asaf Department of Pediatrics, Children Hospital and Institute of Child Health, Lahore Pakistan
Muhammad Asim Khan Department of Pediatrics, Children Hospital and Institute of Child Health, Lahore Pakistan
Tehmina Kazmi Department of Pediatrics, Children Hospital and Institute of Child Health, Lahore Pakistan
Uzma Kazmi Department of Pediatrics, Children Hospital and Institute of Child Health, Lahore Pakistan

DOI:

https://doi.org/10.51253/pafmj.v74i3.5464

Keywords:

Aortic Insufficiency, Double Chambered Right Ventricle, Mid Cavity Right Ventricular Outflow Tract Obstruction, Right Coronary Cusp Prolapse

Abstract

Objective: To identify anatomical features, association and surgical results of patient with double chambered right ventricle.

Study Design: Prospective longitudinal study.

Place and Duration of Study: The Children Hospital and Institute of Child Health, Lahore Pakistan, from Jan 2013 to Dec 2018.

Methodology: All patients presenting with mid cavity right ventricular outflow tract obstruction were included. All patients’ demographic data, clinical profile, diagnostic reports, associated anomalies, and surgical data were recorded.

Results: Fifty-two patients with mid-cavity right ventricular outflow tract obstruction of various ages (from 6 months to 31 years) were included. Ten patients (19%) presented in infancy. Forty-six patients (89%) had an associated ventricular septal defect, ten (15%) had aortic valve right coronary cusp prolapse with varying degrees of aortic regurgitation. All patients had a right ventricular mid-cavity and infundibular muscle resection via the tricuspid valve. There was one hospital death due to an intraoperative global neurologic catastrophe. The median follow-up after surgery was 37.5 months. There was no late death.

Conclusion: Doubly committed Ventricular septal defect with aortic valve right coronary cusp prolapse with varying degree of aortic regurgitation and absence of subaortic stenosis is a new finding in our study. Early and Medium-term surgical results of repair are excellent.

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