BUDD CHIARI SYNDROME

Abstract

Budd Chiari Syndrome (BCS) is an uncommon condition first described by Budd and then expounded upon by Chiari. In this syndrome there is hepatic venous outflow obstruction, which usually occurs at the level of inferior vena cava, the hepatic veins and depending on the classification and nomenclature, possibly at the venule level. There are two types of BCS: acute and chronic [1]. The acute form results from an acute thrombosis of the main hepatic veins or the inferior vena cava (IVC). The chronic form is related to fibrosis of the intrahepatic veins, presumably related to inflammation. The classical presentation is with ascites, hepatomegaly and abdominal pain.