APLASIA CUTIS CONGENITA

Abstract

INTRODUCTION

Aplasia cutis congenital (ACC) is a rare congenital anomaly characterized by partial or complete absence of the skin¹. This disorder was first described by Cordon in 1767 in the extremities and in scalp by Campbell in 1862². Association of ACC with distal limb anomalies was demonstrated by Adams-Oliver in 1945³. Various subtypes are explained on the basis of modes of inheritance, associated malformations, pattern of lesions and their location⁴. The condition has an incidence of 3 per 10000 live births and in 70% of cases occurs as a solitary lesion but may present as multiple lesions with involvement of different body parts⁵.