HERLYN-WERNER-WUNDERLICH SYNDROME-ROLE OF IMAGING IN TIMELY AND CORRECT DIAGNOSIS

Hidayat Ullah; Atiq Ur Rehman Slehria; Rashid Mahmood; Jehan Akbar

doi:10.51253/pafmj.v71i1.3740

Authors

Hidayat Ullah Frontier Medical College Abbottabad Pakistan
Atiq Ur Rehman Slehria Armed Forces Institute of Radiology & Imaging/National University of Medical Sciences (NUMS) Rawalpindi Pakistan
Rashid Mahmood Combined Military Hospital/National University of Medical Sciences (NUMS) Rawalpindi Pakistan
Jehan Akbar Akbar Medical Center Sawabi Pakistan

DOI:

https://doi.org/10.51253/pafmj.v71i1.3740

Keywords:

Herlyn Werner Wunderlich syndrome, OHVIRA, Renal agenesis, Uterus didelphys, Haematometrocolpos, Müllerian duct anomalies

Abstract

We present this case of uterus didelphys with right sided haematometrocolpos due to obstructed hemivagina
and ipsilateral renal agenesis-Herlyn Werner Wunderlich syndrome. The condition was missed on ultrasound
and diagnosed on plain CT scan abdomen and pelvis. This syndrome should be kept in mind while dealing with
a young female complaining of lower abdominal pain and a pelvic mass having unilateral renal agenesis and an
ipsilateral pelvic cystic lesion on ultrasound or other imaging modality. Timely diagnosis is important to avoid
complications like pyocolpos and retrograde spilling of blood with consequent endometriosis. Imaging plays a
major role in a correct and timely diagnosis.